Autoimmune Inner Ear disease (AIED) is a condition in which the body’s immune system mistakenly attacks cells in the inner ear, which causes inflammation. Symptoms may include: sudden hearing loss (usually starting in one ear and spreading to the other), vertigo, and ringing, hissing, or roaring sounds in the ear. Seventy nine percent of patients experience hearing loss in both ears. AIED occurs in both men and women, but is more common in women. The average age of onset is between 20 and 50 years old, and cases in young children are uncommon. AIED can be diagnosed using tests to assess hearing loss or loss of balance, in addition to blood tests for general autoimmune diseases. Treatment may include use of steroids or hearing aids, gene therapy, or cochlear implant.