Biliary Atresia Extrahepatic

Common Name(s)

Biliary Atresia Extrahepatic

Biliary atresia is a disorder of infants in which there is progressive obliteration or discontinuity of the extrahepatic biliary system, resulting in obstruction of bile flow. Untreated, the resulting cholestasis leads to progressive conjugated hyperbilirubinemia, cirrhosis, and hepatic failure ({1:Bates et al., 1998}). Most patients require liver transplantation within the first year of life ({9:Leyva-Vega et al., 2010}). See also Alagille syndrome ({118450}), which includes biliary atresia as a feature.
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Biliary Atresia Extrahepatic" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Biliary Atresia Extrahepatic" returned 24 free, full-text research articles on human participants. First 3 results:

Infants with extrahepatic biliary atresia: Effect of follow-up on the survival rate at Ege University Medical School transplantation center.
 

Author(s): Miray Karakoyun, Maşallah Baran, Caner Turan, Murat Kılıç, Orkan Ergun, Sema Aydoğdu

Journal: Turk J Gastroenterol. 2017 Jul;28(4):298-302.

 

Biliary atresia (BA) is the main cause of neonatal cholestasis and the primary reason for infant liver transplants worldwide. It is an obliterative cholangiopathy observed only in children and caused by progressive inflammation and fibrosis of the bile duct. We collaborated with a ...

Last Updated: 31 Dec 1969

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Diagnostic value of anti-smooth muscle antibodies and liver enzymes in differentiation of extrahepatic biliary atresia and idiopathic neonatal hepatitis.
 

Author(s): Mandana Rafeey, Lida Saboktakin, Jamshid Shoa Hasani, Shahnaz Naghashi

Journal: Afr J Paediatr Surg. ;13(2):63-8.

 

We aimed to evaluate the diagnostic value of anti-smooth muscle antibodies (ASMA) and two liver markers (gamma-glutamyl transpeptidase [GGT] and alkaline phosphatase [ALP]) for differentiating between patients with extrahepatic biliary atresia (EHBA) and idiopathic neonatal hepatitis (INH).

Last Updated: 31 Dec 1969

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Biliary Atresia Extrahepatic" returned 3 free, full-text review articles on human participants. First 3 results:

Extrahepatic biliary atresia: current concepts and future directions.
 

Author(s): Elisa de Carvalho, Cláudia Alexandra Pontes Ivantes, Jorge A Bezerra

Journal: J Pediatr (Rio J). ;83(2):105-20.

 

To provide an updated review on extrahepatic biliary atresia, focusing mainly on its etiopathogenesis, diagnosis, treatment and prognosis.

Last Updated: 31 Dec 1969

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[Extrahepatic biliary atresia: diagnostic methods].
 

Author(s): Sydney M Cauduro

Journal: J Pediatr (Rio J). ;79(2):107-14.

 

To emphasize the importance of precocious diagnosis of extrahepatic biliary atresia and its direct relationship with the surgical re-establishment of the biliary flow before the second month of life. To discuss several complementary methods with the aim of selecting the ones that ...

Last Updated: 31 Dec 1969

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Extrahepatic biliary atresia. Recent developments in management.
 

Author(s): E R Howard, A P Mowat

Journal: Arch. Dis. Child.. 1977 Nov;52(11):825-7.

 

Last Updated: 31 Dec 1969

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