Budd-Chiari Syndrome

Common Name(s)

Budd-Chiari Syndrome

Budd-Chiari syndrome is a rare disorder characterized by narrowing and obstruction of the veins of the liver. This narrowing or obstruction slows or prevents blood from flowing out of the liver and back to the heart which can lead to liver damage. While some people experience no symptoms, many experience fatigue, abdominal pain, nausea, and jaundice. Other associated findings include an accumulation of fluid in the abdomen (ascites), an enlarged spleen and/or liver, and severe bleeding in the esophagus. The severity of the disorder varies from case to case, depending on the site and number of affected veins. Drugs may be used to dissolve or decrease the size of the obstruction (if it is a clot). In some cases surgery is performed.  In most cases, the cause of Budd-Chiari syndrome is unknown.
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Budd-Chiari Syndrome" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Budd-Chiari Syndrome" returned 282 free, full-text research articles on human participants. First 3 results:

New Left Lobe Transplantation Procedure with Caval Reconstruction Using an Inverted Composite Graft for Chronic Budd-Chiari Syndrome in Living-Donor Liver Transplantation-A Case Report.
 

Author(s): T Yagi, K Takagi, R Yoshida, Y Umeda, D Nobuoka, T Kuise, T Fujiwara, A Takaki

Journal: Transplant. Proc.. 2018 May;50(4):1192-1195.

 

When the Budd-Chiari syndrome (BCS) lesion extends to the inferior vena cava (IVC) or the orifices of the hepatic vein, the thickened IVC and/or hepatic vein wall must be removed and IVC reconstruction is required in living-donor liver transplantation (LDLT). In various reports about ...

Last Updated: 31 Dec 1969

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Budd-Chiari syndrome in China: A 30-year retrospective study on survival from a single center.
 

Author(s): Wei Zhang, Qiao-Zheng Wang, Xiao-Wei Chen, Hong-Shan Zhong, Xi-Tong Zhang, Xu-Dong Chen, Ke Xu

Journal: World J. Gastroenterol.. 2018 Mar;24(10):1134-1143.

 

To investigate 30-year treatment outcomes associated with Budd-Chiari syndrome (BCS) at a tertiary hospital in China.

Last Updated: 31 Dec 1969

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Budd-Chiari Syndrome Diagnosed in a Patient Listed for Liver Transplant and Considered to be Contraindicated for the Operation.
 

Author(s): Kakharman Yesmembetov, Zhansaya Muratova, Sergey Borovskiy, Irina Ten, Kulpash Kaliaskarova

Journal: Exp Clin Transplant. 2018 Mar;16 Suppl 1(Suppl 1):158-161.

 

We report the clinical case of 23-year-old patient with liver cirrhosis of unknown genesis, significant resistant ascites, and 2 episodes of bleeding from esophageal varices. Evaluation did not find any cause of liver disease, and the patient was placed on the transplant wait list ...

Last Updated: 31 Dec 1969

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Budd-Chiari Syndrome" returned 22 free, full-text review articles on human participants. First 3 results:

Review article: the aetiology of primary Budd-Chiari syndrome - differences between the West and China.
 

Author(s): X Qi, G Han, X Guo, V De Stefano, K Xu, Z Lu, H Xu, A Mancuso, W Zhang, X Han, D C Valla, D Fan

Journal: Aliment. Pharmacol. Ther.. 2016 12;44(11-12):1152-1167.

 

China may have the largest number of Budd-Chiari syndrome (BCS) cases in the world (at least 1914 original papers were published, and at least 20 191 BCS patients were reported). Considering the discrepancy in the clinical profiles and preferred treatment selection of primary BCS ...

Last Updated: 31 Dec 1969

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Budd-chiari syndrome causing acute liver failure: A multicenter case series.
 

Author(s): Justin Parekh, Vlad M Matei, Alejandro Canas-Coto, Daniel Friedman, William M Lee,

Journal: Liver Transpl.. 2017 02;23(2):135-142.

 

Budd-Chiari syndrome (BCS) is a rare disease resulting from obstruction of the hepatic venous outflow tract that typically presents with abdominal pain, jaundice, and ascites without frank liver failure. However, BCS may also evolve more rapidly to acute liver failure (ALF). In this ...

Last Updated: 31 Dec 1969

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Budd-Chiari syndrome: current perspectives and controversies.
 

Author(s): L Liu, X-S Qi, Y Zhao, H Chen, X-C Meng, G-H Han

Journal: Eur Rev Med Pharmacol Sci. 2016 07;20(15):3273-81.

 

Budd-Chiari syndrome (BCS) is a rare disorder caused by hepatic venous outflow obstruction with a wide spectrum of etiologies. Clinical manifestations are so heterogeneous that the diagnosis should be considered in any patients with acute or chronic liver disease. Therapeutic modalities ...

Last Updated: 31 Dec 1969

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Vienna Vascular Liver Disease Study
 

Status: Recruiting

Condition Summary: Vascular Liver Disease; Portal Vein Thrombosis; Budd-Chiari Syndrome; Non-Cirrhotic Portal Hypertension; Rendu Osler Weber; Cardiac Cirrhosis

 

Last Updated: 17 May 2018

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