Dextrocardia

Common Name(s)

Dextrocardia

Dextrocardia is a group of rare heart defects present at birth (congenital). The simplest type occurs when the heart is a mirror image of a normal heart and still functions correctly. Usually the other organs of the body are also in mirror image, but again all organs work correctly. Sometimes babies with dextrocardia also have a problem with the fine hair (cilia) found in the nose and air passages (Kartagener syndrome). More commonly, dextrocardia is found with other heart defects including double outlet right ventricle, endocardial cushion defect, pulmonary atresia, single ventricle, transposition of the great vessels, or ventricular septal defects. Heterotaxy may also be present which is when the organs of the baby are not in the right place and do not work properly.

Symptoms depend on the type of dextrocardia and other birth defects present. If the heart is a complete mirror image, no symptoms may be present. If the condition is more complicated, symptoms may include pale or bluish skin, difficulty breathing, yellowing of the skin or eyes (jaundice), fatigue, slow growth and weight gain, and repeated lung and sinus infections. The cause of dextrocardia is unknown but it can run in families.

Tests including CT scans, electrocardiogram (EKG), cardiac MRI, echocardiogram (ultrasound of heart) and X-rays can confirm the diagnosis and look for other birth defects. A complete mirror image dextrocardia with no other heart defects will not need treatment. If other defects are present, treatment options, including different types of medications and surgery, will depend on the type and severity of the other defects. Research is ongoing so talk to your baby’s heart doctor and other specialist(s) about the most current treatment options. A genetic counselor and support organizations are good sources of information and can help connect you with other families affected by dextrocardia.

Source: Advocacy organizations associated with the condition.

 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Dextrocardia" for support, advocacy or research.

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General Support Organizations

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Dextrocardia" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Dextrocardia" returned 102 free, full-text research articles on human participants. First 3 results:

Catheter ablation of premature ventricular contractions originating from aortic sinus cusps in a patient with dextrocardia and situs solitus: A case report.
 

Author(s): Chao-Feng Chen, Xiao-Hua Liu, Xiao-Fei Gao, Bin Chen, Yi-Zhou Xu

Journal: Medicine (Baltimore). 2017 Dec;96(48):e8947.

 

Premature ventricular contractions (PVCs) originating from aortic sinus cusps is not infrequent and can be eliminated effectively by radiofrequency ablation with rare complications. However, after a review of the medical literature, and to our knowledge, this is the first case of ...

Last Updated: 31 Dec 1969

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Case 4/2017 - Double-Chambered Right Ventricle with Dextrocardia and Hypoxemia Due to Atrial Shunt in a 4-Year-Old Girl.
 

Author(s): Edmar Atik, José Fernando Cavalini

Journal: Arq. Bras. Cardiol.. 2017 Jun;108(6):569-571.

 

Last Updated: 31 Dec 1969

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Successful transradial coronary angioplasty in a patient with dextrocardia and acute myocardial infarction.
 

Author(s): George Michas, Ioannis Kaplanis, Pavlos Stougiannos, Sophia Arapi, Evelina Sergi, Gerasimos Gavrielatos, Athanasios Trikas

Journal: Hellenic J Cardiol. ;57(6):463-466.

 

Last Updated: 31 Dec 1969

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Dextrocardia" returned 5 free, full-text review articles on human participants. First 3 results:

Aeroembolism in left atrium during catheter ablation of atrial fibrillation in a patient with dextrocardia: a case report and review of the literature.
 

Author(s): Yun-Fan Wang, Xue-Jiang Cen, Jian-Wu Yu, Bai-Ming Qu, Li-Hong Wang

Journal:

 

Air embolus penetrating into heart chamber as a complication during percutaneous radiofrequency catheter ablation has been infrequently reported.

Last Updated: 31 Dec 1969

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Tetralogy of fallot with dextrocardia and situs inversus in a 7-year-old boy.
 

Author(s): Michael Dilorenzo, Samuel Weinstein, Rajesh Shenoy

Journal: Tex Heart Inst J. 2013 ;40(4):481-3.

 

Tetralogy of Fallot is one of the most frequently diagnosed congenital cardiac abnormalities; however, its association with dextrocardia and situs inversus is reported only rarely. We report a case of these findings in a 7-year-old boy, describe the patient's postoperative course, ...

Last Updated: 31 Dec 1969

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Endovascular repair of blunt aortic injury in a patient with situs inversus and dextrocardia.
 

Author(s): John F Bilello, Peter L Birnbaum, Chandra Venugopal, Leo L Fong

Journal: J. Vasc. Surg.. 2011 Sep;54(3):857-9.

 

A 24-year-old male pedestrian with situs inversus and dextrocardia was struck by a car and sustained multiple injuries, including a pseudoaneurysm of the proximal descending thoracic aorta. A thoracic endograft was deployed to exclude the blunt aortic injury. We are not aware of any ...

Last Updated: 31 Dec 1969

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
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Clinical Trial Information This information is provided by ClinicalTrials.gov

Ambrisentan in Single Ventricle
 

Status: Recruiting

Condition Summary: Hypoplastic Left Heart Syndrome; Hypoplastic Right-sided Heart Complex

 

Last Updated: 2 May 2017

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Spironolactone Therapy in Chronic Stable Right HF Trial
 

Status: Not yet recruiting

Condition Summary: Chronic Right-Sided Heart Failure; Pulmonary Arterial Hypertension; Pulmonary Hypertension, Primary, 2; Pulmonary Hypertension, Primary, 3; Pulmonary Hypertension, Primary, 4; Cardiomyopathy Right Ventricular

 

Last Updated: 14 Nov 2017

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Last Updated: 12 Jan 2018

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