Hemangioendothelioma

Common Name(s)

Hemangioendothelioma

The term hemangioendothelioma describes several types of vascular neosplasms and includes both non-cancerous (benign) and cancerous (malignant) growths. The term has also been applied to those that show "borderline" behavior, intermediate between entirely benign hemangiomas and highly malignant angiosarcomas. Hemangioendotheliomas are caused by abnormal growth of blood vessel cells, although the exact underlying cause for the abnormal growth is unknown. They can also develop in an organ, such as the liver or lung. They usually grow slowly and can sometimes spread to other tissues in the body (metastasize). Examples of types of hemangioendotheliomas include spindle cell hemangioma; papillary intralymphatic (Dabska tumor); retiform; kaposiform; epithelioid; pseudomyogenic (epithelioid sarcoma-like hemangioendothelioma); and composite. Treatment depends on the type of hemangioendothelioma present but typically includes surgical excision (removal).
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Hemangioendothelioma" for support, advocacy or research.

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General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Hemangioendothelioma" returned 179 free, full-text research articles on human participants. First 3 results:

Diffuse hepatic epithelioid hemangioendothelioma with multiple splenic metastasis and delayed multifocal bone metastasis after liver transplantation on FDG PET/CT images: A case report.
 

Author(s): Yanlin Tan, Xiaohuang Yang, Chuning Dong, Zhe Xiao, Hongbo Zhang, Yunhua Wang

Journal: Medicine (Baltimore). 2018 Jun;97(22):e10728.

 

Malignant hepatic epithelioid hemangioendotheliom (HEH) is a rare vascular tumor of endothelial origin, with multiple metastases to the spleen. This report describes a diffuse HEH with splenic metastasis on 18F-fluorodeoxyglucose (18F-FDG) positron emission tomography/computed tomography ...

Last Updated: 31 Dec 1969

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Pseudomyogenic (epithelioid sarcoma-like) hemangioendothelioma - a rare vascular neoplasm with deceptive morphology and distinctive immunophenotype.
 

Author(s): F F Cheo, K Sittampalam

Journal: Malays J Pathol. 2017 Dec;39(3):305-309.

 

Pseudomyogenic (epithelioid sarcoma-like) hemangioendothelioma is a rare, low grade vascular (endothelial) neoplasm typically presenting as multicentric, superficial to deep nodules in extremities with a slight tendency of affecting young adult males. We report a case of pseudomyogenic ...

Last Updated: 31 Dec 1969

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Intravascular epithelioid hemangioendothelioma of the femoral vein diagnosed by contrast-enhanced ultrasonography: A care-compliant case report.
 

Author(s): Luying Gao, Yahong Wang, Yuxin Jiang, Xingjian Lai, Ming Wang, Jianchu Li

Journal: Medicine (Baltimore). 2017 Dec;96(49):e9107.

 

Intravascular epithelioid hemangioendothelioma (EHE) is a rare endothelial tumor with an intermediate grade of malignancy. We present a case of one woman affected by EHE of the femoral vein. Contrast-enhanced ultrasonography played a role in diagnosing EHE and helped differentiate ...

Last Updated: 31 Dec 1969

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Hemangioendothelioma" returned 22 free, full-text review articles on human participants. First 3 results:

Clinico-radiological features and next generation sequencing of pulmonary epithelioid hemangioendothelioma: A case report and review of literature.
 

Author(s): Xiaoyong Mao, Zibin Liang, Fidelis Chibhabha, Wei Ou, Ning Li, Pengfei Xu, Siyu Wang

Journal: Thorac Cancer. 2017 11;8(6):687-692.

 

Epithelioid hemangioendothelioma is a very rare, vascular, low-grade malignant tumor found in the lungs, liver, bone, and other soft tissues. Most patients with pulmonary epithelioid hemangioendothelioma (PEH) are asymptomatic but usually present with multiple bilateral nodular lesions ...

Last Updated: 31 Dec 1969

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Spontaneous rupture of hepatic epithelioid hemangioendothelioma: A case report.
 

Author(s): Jun-Wu Yang, Yong Li, Kai Xie, Wei Dong, Xian-Tong Cao, Wei-Dong Xiao

Journal: World J. Gastroenterol.. 2017 Jan;23(1):185-190.

 

Hepatic epithelioid hemangioendothelioma (HEH) is a rare tumor of vascular endothelial origin. Spontaneous rupture of HEH is a life-threatening complication and is extremely rare. HEH has variable malignant potential, and the clinical diagnosis remains challenging. Here we report ...

Last Updated: 31 Dec 1969

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Recurrence of Epithelioid Hemangioendothelioma during Pregnancy: Case Report and Systematic Review.
 

Author(s): Michael Mcculloch, Michael Russin, Arian Nachat

Journal: Perm J. 2016 ;20(3):84-9.

 

Epithelioid hemangioendothelioma (EHE) is a family of blood vessel tumors originating in blood vessels, bone, brain, kidney, liver, and lung. EHE is more common in women, and chemotherapy, radiation, and surgery have brought few successes.

Last Updated: 31 Dec 1969

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Eribulin in Angiosarcoma and Epithelioid Hemangioendothelioma (EHE)
 

Status: Recruiting

Condition Summary: Angiosarcoma; Epithelioid Hemangioendothelioma

 

Last Updated: 9 Aug 2018

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Sirolimus Plus Propranolol Versus Sirolimus Plus Prednisolone for Kaposiform Hemangioendothelioma
 

Status: Recruiting

Condition Summary: Kaposiform Hemangioendothelioma; Kasabach Merritt Phenomenon

 

Last Updated: 17 Jun 2018

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A Study to Compare Vincristine to Sirolimus for Treatment of High Risk Vascular Tumors
 

Status: Recruiting

Condition Summary: Kaposiform Hemangioendothelioma (KHE); Kasabach-Merritt Syndrome; Tufted Angioma

 

Last Updated: 16 Aug 2018

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