Meningoencephalocele

Common Name(s)

Meningoencephalocele

Meningoencephalocele is a type of encephalocele, which is an abnormal sac of fluid, brain tissue, and meninges (membranes that cover the brain and spinal cord) that extends through a defect in the skull.  There are two main types of meningoencephalocele, which are named according to the location of the sac. The frontoethmoidal type is located at the frontal and ethmoid bones while the occipital type is located at the occipital bone.  Hydrocephalus, abnormalities of the eyeball and tear duct, and other findings have been associated with the condition.  Some affected individuals have intellectual or physical disabilities while others have normal development and abilities.  The condition is typically congenital (present at birth) but has been reported to develop by chance in older individuals in rare cases. The underlying cause of the condition is uncertain, but environmental factors are thought to play a role. Treatment depends on the size, location and severity of the defect but mainly includes magnetic resonance imaging (MRI) to determine the severity of the defect, followed by surgery to repair it.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Meningoencephalocele" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
Top

How do you compare to others with this condition?

Privately answer questions about your health. Let resources, you select, come to you.

Anonymously share and see how your answers compare with others with this condition while privately providing key pieces of information to medical researchers, disease advocacy groups, and others ONLY YOU select to help speed up cures and better alternatives.

 
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Meningoencephalocele" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
 
 
Top

Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Meningoencephalocele" returned 17 free, full-text research articles on human participants. First 3 results:

[Endoscopic endonasal diagnosis and treatment of skull base meningoencephalocele].
 

Author(s): D N Kapitanov, E V Shelesko, A A Potapov, A D Kravchuk, D N Zinkevich, M V Nersesyan, L A Satanin, A V Sakharov, G V Danilov

Journal: Zh Vopr Neirokhir Im N N Burdenko. ;81(2):38-47.

 

The study purpose was to determine the successful outcome rate of endoscopic endonasal reconstruction of skull base CSF fistulas with removal of meningocele as well as analyze disease relapses. The second purpose of the study was to describe the treatment outcomes, depending on the ...

Last Updated: 31 Dec 1969

Go To URL
Transalar transsphenoidal meningoencephalocele presenting in the form of recurrent meningitis: Report of two cases and discussion of the diagnosis and treatment.
 

Author(s): A Zoghlami, N Bon Mardion, F Callonnec, D Dehesdin, F Proust, J-P Marie

Journal: Eur Ann Otorhinolaryngol Head Neck Dis. 2016 Dec;133(6):423-427.

 

Skull base meningoencephaloceles are rare congenital malformations. The two cases of transalar transsphenoidal malformation reported here differ from the classical transsphenoidal meningoencephalocele.

Last Updated: 31 Dec 1969

Go To URL
Comments on "Endoscopic Transpterygoid Approach and Skull Base Repair After Sphenoid Meningoencephalocele Resection".
 

Author(s): Nathaniel Reeve, Bradford A Woodworth

Journal: Acta Otorrinolaringol Esp. ;67(1):58.

 

Last Updated: 31 Dec 1969

Go To URL

Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Meningoencephalocele" returned 2 free, full-text review articles on human participants. First 3 results:

Transcranial approach for spontaneous CSF rhinorrhea due to Sternberg's canal intrasphenoidal meningoencephalocele: case report and review of the literature.
 

Author(s): Mohammad Samadian, Habibollah Moghaddasi, Mohsen Vazirnezami, Karim Haddadian, Omidvar Rezaee, Mehran Armanfar, Fatemeh Khormaee

Journal: Turk Neurosurg. 2012 ;22(2):242-5.

 

One type of congenital intrasphenoidal meningoencephalocele is remnant of lateral craniopharyngeal (Sternberg's) canal. We present a case of a 23-year girl with 10-month history of right side CSF rhinorrhea. CT scan, MRI revealed congenital meningoencephalocele and CSF ...

Last Updated: 31 Dec 1969

Go To URL
Transethmoidal meningoencephalocele in an elderly woman. Case report.
 

Author(s): Atsuhiko Kubo, Katsumi Sakata, Jiro Maegawa, Isao Yamamoto

Journal: Neurol. Med. Chir. (Tokyo). 2005 Jun;45(6):322-6.

 

A 69-year-old woman presented with a transethmoidal meningoencephalocele manifesting as gradually developing anosmia. Examinations revealed a mass in the nasal cavity associated with multiple angiomas in her lip and orbit. Neuroimaging showed meningoencephalocele extending via the ...

Last Updated: 31 Dec 1969

Go To URL
 
 
Top

Symptoms, Diagnosis, and Treatment

There are currently no related results available in Genetics Home Reference.

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
Top

Clinical Trial Information This information is provided by ClinicalTrials.gov

There are currently no open clinical trials for this condition.